Lect 13 optic neuropathies 4 Flashcards
Which one of the following is NOT true regarding Optic Nerve Hypoplasia?
a) pt may also have absent/poorly developed corpus callosum and/or septum pellucidum
b) associated findings include: ocular coloboms, strabismus, hypertelorism, micropthalmos, and aniridia
c) fundoscopy shows double ring sign
d) VF defects show enlarged blind spot
d) VF defects show enlarged blind spot (FALSE, VF defects are altitudinal, arcuate, and temporal depressions)
(T/F) DeMorsiers syndrome is also known as septo-optic dysplasia
true
Which one of the following is NOT true regarding DeMorsiers syndrome?
a) typical late onset after 50 yrs old
b) pt has optic nerve hypoplasia
c) pt has pituitary hypoplasia
d) abnormal formation of midline brain structures (corpus callosum and septum pellucidum)
a) typical late onset after 50 yrs old (FALSE, it is a disorder of early brain development)
Which one of the following is NOT true regarding optic nerve pit?
a) stable arcuate VF defects may be present
b) may lead to macular edema
c) usually found in superior temporal aspect of ONH
d) all of the above are true
c) usually found in superior temporal aspect of ONH (FALSE, its found in infero-temporal aspect of ONH)
Which one of the following is NOT true regarding Morning Glory syndrome?
a) unilateral with OD more common
b) found mostly in males
c) white tuft of glial tissueoverlies central portion of enlarged disc
d) funnel shaped excavation of posterior fundus including the optic nerve
e) no known hereditary pattern
b) found mostly in males (FALSE, more in females)
Which one of the following is NOT one of the cardinal signs of Morning Glory syndrome?
a) cup is enlarged with deep depression and white glial tissue at the base
b) raised annulus surrounds disc with variable amount of pigment
c) retinal blood vessels emerge from disc in radial fashion, like spokes on a wheel
d) situs inversus: blood vessels directed nasally before sweeping temporally
d) situs inversus: blood vessels directed nasally before sweeping temporally (NO, this describes tilted disc)
Match the following characteristics with the folloowing disorders:
1) Morning glory
2) ONH coloboma
a) significant PPA
b) no PPA
c) normal retinal vasculature
d) anomalous retinal vasculature
e) optic disc lies within excavation
f) excavation lies within optic disc
g) central glial tuft
h) no central glial tuft
i) usually unilateral
j) unilateral or bilateral
1) Morning glory
a) significant PPA
d) anomalous retinal vasculature (spoke-like)
e) optic disc lies within excavation
g) central glial tuft
i) usually unilateral
(colobomas uncommon)
2) ONH coloboma
b) no PPA
c) normal retinal vasculature
f) excavation lies within optic disc
h) no central glial tuft
j) unilateral or bilateral
What is the term for enlarged optic disc greater than 2.2 mm without additional morphological abnormalities?
megalopapilla
Which one of the following is NOT true regarding tilted disc syndrome?
a) situs inversus: blood vessels directed nasally before sweeping temporally
b) high myopic astigmatism with oblique axis
c) VF loss has superior bitemporal appearance
d) caused by oblique insertion of optic nerve into the globe
e) all of the above are correct
e) all of the above are correct (also, supero-temporal optic disc is elevated, infero-nasal optic disc is posteriorly displaced)
Which one of the following is NOT true related to psuedopapilledema?
a) anomalous BV: multiple bifurcations, trifucations
b) optic nerve drusen: hyaline bodies anterior to LC
c) typical VF defects are central and ceco-central
d) small scleral opening for axons to squeeze through
c) typical VF defects are central and ceco-central (FALSE, VF defect is typically arcuate and can be progressive)
Match the following conditions with their characteristics:
1) pseudopapilledema
2) papilledema
a) swelling greatest in center
b) swelling greatest at edges
c) normal bifurcations
d) anomalous bifurcations
e) may/may not have SVP
f) no SVP
g) RNFL hemes common
h) RNFL hemes not common
i) no genetic component
j) familial
1) pseudopapilledema
a) (pseudo) swelling greatest in center
d) anomalous bifurcations
e) may/may not have SVP
h) RNFL hemes not common
j) familial
2) papilledema
b) swelling greatest at edges
c) normal bifurcations
f) no SVP
g) RNFL hemes common
i) no genetic component
Which combination of pattern of VF loss does NOT match?
a) central scotoma: NAION
b) bitemporal: parasellar lesions
c) hemianopic: ischemic/compressive
d) centro-cecal: toxic/nutritionall/DOA
a) central scotoma:NAION (FALSE: NAION is altitudinal)
Which one of the following is not associated with optociliary shunt vessels?
a) CRVO
b) chronic glaucoma
c) optic nerve sheath meningioma
d) optic nerve glioma
d) optic nerve glioma
Which one of the following is NOT associated with temporal pallor?
a) dominant optic atrophy
b) toxic optic atrophy
c) nutritional optic atrophy
d) infectious optic neuropathy
d) infectious optic neuropathy
