Interstitial Lung Disease Flashcards
Best initial Test for Pulmonary Fibrosis
Chest X-ray
Most accurate test for pulmonary fibrosis
Lung Biopsy
-shows granulomas in Berylliosis
PFT results for Pulmonary Fibrosis
Restrictive pattern
-decreased FEV1
-decreased FVC
-decreased TLC
-decreased Residual Volume
-Normal FEV1/FVC ratio
Treatment for Pulmonary Fibrosis
Steroids
-use Azathioprine long-term
Pirfenidone
-inhibits collagen synthesis
Nintedanib
-blocks fibrogenic growth factors
Best initial Test for Sarcoidosis
Chest X-ray
-hilar lymphadenopathy
-parenchymal involvement
-Lymphadenopathy
Most accurate test for sarcoidosis
Node Biopsy
-noncaseating granulomas
PFT in sarcoidosis
Restrictive pattern
Treatment for Sarcoidosis
Prednisone: Drug of choice
Best initial Test for Pulmonary Hypertension
Chest X-ray and CT
-Dilation of proximal pulmonary arteries
-narrowing of distal vessels “Pruning”
Most accurate test for Pulmonary Hypertension
Right heart/Swan-Ganz Catheter
Treatment for Pulmonary Hypertension
Prostacyclin: dilate Pulmonary Artery
Endothelin Antagonists
PDE-inhibitors
cGMP stimulants
Calcium channel Blockers
Oxygen to slow progression
Lung Transplant
Most accurate test for BOOP/COP
Lung Biopsy
Treatment for BOOP/COP
Glucocorticoids
Diagnosis for Hypersensitivity Pneumonitis
Chest CT and Chest X-ray
-Bilateral hazy opacities
Treatment for Hypersensitivity Pneumonitis
Glucocorticoids
Most accurate test for Eosinophilic Pneumonia
Eosinophils on BAL or Lung Biopsy
Treatment for Eosinophilic Pneumonia
Steroids