Heme part 1 Flashcards
An x-linked recessive disorder transmitted by females and predominantly found in male offsprings
Haemophilia, in this disease, a group of bleeding disorders characterized by a deficiency in a blood clotting factor
Cara just delivered a baby that has excessive bleeding from the umbilical cord after it is cut. What disease do you think this newborn has?
Haemophilia. The nurse should also assess for bruising, nose bleeds, deep internal bleeding, and joint damage.
Haemophilia mangement includes:
meds (Factor VIII, Advate for Factor XI), DDAVP (increases the level of factor VIII), medic-alert bracelet, injury prevention, reg. dental diet, and no aspirin or aspiring like meds
Scotty, a 6 year old was recently diagnosed with Hemophilia. As his nurse, what are you going to educate mom about?
ANY head trauma= factor infusion, bleeding episodes need immediate attention, limitation in sports but encourage reg. exercise, make sure child wears medic-alert bracelet, and no aspirin or aspirin-like meds
Peety Pablo comes into the ED complaining of a headache when he work up, blurry vision and vomiting. He denies nausea though. What could he possible have?
Brain tumor. Patients with brain tumors typically will have a headache when awakening, vomiting without nausea, loss of concentration, change in behavior and vision problems
1 disease related death in children
Cancer
Most common childhood cancer
leukemia
Most common solid tumor
brai
What is the most common presenting symptom of brain tumors
headache on awakening
Pain, fever, weakness, cachexia, anemia, persisten vomiting, headache, infection, and bruising are all what?
Clinical presentations of brain tumors
In an assessment of a infant with a brain tumor, what might you find?
widening sutures, increasing frontal occipital circumference, and tense/buldging fontanel
Post op care for brain tumor includes:
observing for increased ICP and seizures, monitor I and O, and appropriate post-op positioning
While monitoring I and O, what are you specifically looking out for?
SIADH and DI
Upon assessment, your patinet has voided a large amount of dilute urine. Since he is post-op brain tumor removal, what might this patient be exhibiting?
Diabetes insipidus caused by a deficiency in antidiuretic hormon. When ADH is inadequate, the renal tubules do not absorb water, leading to polyuria
Most postop clients with infratentorial (lower portion of back of the head) tumors are prescribed to:
lie flat or turn to either side
T or F, a large tumor may require that the child not be turned to the operative side
TRUE
Suctioning, coughing, and straining can all cause :
increased ICP
Malignant, encapsulated renal tumor
Wilm’s Tumor- usually affects young, preschoolers
Clinical manifestations of Wilm’s tumor include:
abdominal mass in flank area, confided to midline (usually discovered by parents), fever, pallor, lethargy, ^ BP (excess renin secretion)
You are the nursing caring for 5 year old Billie who has a Wilm’s Tumor. What should you make sure you NEVER do to this patient?
NO abdominal palpation
Most kids with Wilm’s Tumor undergo a nephrectomy, what is included in their post-op care?
Watch for ^ BP, monitor kidney function (I & O, urine specific gravity), maintain NG tube, check for bowel sounds, and support family during chemo and radiation
This form of childhood cancer attacks the developing nerve cells in the adrenal gland
Neuroblastoma also called the “Silent Tumor”
Onset of Neurblastoma
22 months of age
Clinical manifestations of Neuroblastoma
May have weight loss, irritability, and fever.
