Gastrointestinal disorders Flashcards
▪ Protrusion of intraabdominal contents through defect in abdominal wall lateral to umbilical ring which is
never with a peritoneal sac
▪ M. membranes covers the exposed
GASTROSCHISIS
Incomplete fusion of the palate which results in
communication between the mouth and the nose
Cleft Palate
when will cleft palate precede cleft lip
6 – 12 weeks
AE/TEF: A2
Simple esophageal atresia with no fistula (Isolated EA)
signs of Esophageal motility disorders
dysphagia, GER (50%)
- non union of the tissue and bone of the upper lip and hard/soft palate during embryonic development
- Distinct facial defects that occurs singly or in combination
- Malformation of the face that may occur individually or together
- Both occur during embryonic development
CLEFT LIP (HARELIP)/CLEFT PALATE
Type of cleft palate: occurs in midline and may involve soft
and hard palate
CP alone
what is ESSR
▪ Enlarge the nipple (long, soft)
▪ Stimulate the suck reflex
▪ Swallow fluid appropriately
▪ Rest =to allow child to finish what has been placed in the mouth
(-) air in the GIT in EA/TEF meaning
EA without TEF
Type of EA/TEF: Both upper and lower ends of esophagus open into the
trachea by a fistula
EA with double TEF
Rule of 10
10gms Hgb?10lbs?10wks
Restraints for cleft palate
▪ Elbow restraint until palate healed (4-
6 weeks)
How to prevent infection in Cleft lip/palate
- Assess v/s
- Cleanse suture line with normal saline/sterile water if ordered
- Cleanse cleft areas by giving 5-15 cc of water after feeding
- loosen crust
aiding in removal - Antibiotic cream as prescribed
- Careful hand washing and sterile technique
Assessment for Transesophageal Atresia (TEF)
a) 3 Cs - choking, coughing, cyanosis
b) Aspiration pneumonia
c) Distended abdomen
Preop preparation of the infant for surgery in omphalocele
NPO, IVF, NGT for decompression
Major Etiology/Causes of Cleft lip/palate
genetics and environmental
Speech impairment in CL/CP
o Insufficient functioning of the muscle of the soft palate and nasopharynx
o Improper tooth alignment-orthodontics
o Hearing loss
CLINICAL MANIFESTATIONS of EA/TEF
- 3 C’s of TEF = choking, coughing, cyanosis (intermittent)→due to aspiration from overflow of secretions from the blind pouch
- copious, fine white frothy bubbles of mucus in the mouth and nose=EA
- increased respiratory distress after feeding
- Distended abdomen-air from trachea passes through the fistula into the stomach
Structural Defects
- Cleft lip/ cleft palate
- Esophageal Atresia with Transesophageal Fistula
- Omphalocele
Protrusion of intraabdominal contents into the base of umbilicus which is covered by a translucent sac
(peritoneum without skin)→rupture→****
evisceration
position for maintaining patent airway in Cleft lip
upright/infant seat position
How to maintain Airway patency in CP/CL
gentle aspiration (NO SUCTIONING=trauma to the site) of mouth and nasopharyngeal
secretions to prevent aspiration and respiratory complications
Gastrointestinal System of the Newborn
- The infant does not have voluntary control over swallowing until 6 weeks old.
- Stomach capacity is small and intestinal motility is greater than in older children.
- Relaxed cardiac sphincter.
- Deficiency of several enzymes until 4 to 6 months.
- Liver junctions are immature until the first year of life.
How to optimize nutrition in Cleft lip
Rubber tipped syringe on the side of the mouth
incidence of cleft palate
1:2000 live births
week of Fusion of palatal processes
7 – 12th wk AOG
stomach capacity of 2-3 weeks
75-100 ml
postop preparation of the infant for surgery in omphalocele
measures to control pain, prevent infection, fluid and electrolyte balance,
adequate nutritional intake
Gastrostomy tube feedings are elevated and secured to a point above the level of the stomach in how many inches to prevent reflux to the healing esophagus; allows gastric secretions to pass duodenum and swallowed air to escape through open tube
4”
Type of cleft lip: small notch; maybe a little
more than a notching of the vermillion border of the lip and may extend to the nostril
Incomplete
management of EA/TEF
- Prevention of aspiration pneumonia through drug therapy
* →inevitable and appear early
* Broad spectrum antibiotic - Surgery
▪ to repair anomaly→ emergency; closing the fistula and anastomosing esophageal
segments (NGT for feeding until esophagus heals; chest tube)
diagnosis of cleft lip
apparent at birth – detected by Sonogram (while in Utero)
How to protect sac from trauma and infection in omphalocele
▪ Monitor sac and make sure that it is covered with sterile gauze soaked in NSS to prevent drying of abdominal contents
▪ Place dried sterile gauze over sterile moist gauze and cover with plastic wrap to provide additional protection from heat and moisture loss
▪ Monitor vital signs especially temperature because the infant easily loses heat through sac
▪ Monitor for s/s of infection
Pediatric Nursing Gastrointestinal Disorders
A. Structural Defects
B. Disorders of Motility
C. Obstructive Disorders
D. Malabsorption Syndrome
development of larynx, trachea, beginning lung tissue, esophageal
lumen
4th – 8th week
corrective surgeries for EA/TEF
▪ End-to-end anastomosis
▪ Colon transplants for defects
why infant with cleft palate have difficulty feeding
infant is unable to generate a negative pressure and create suction in the oral cavity
incidence of cleft lip
1:800 live births
how to provide adequate nutrition in CL/CP
a. ESSR
b. Upright position when feeding to facilitate swallowing and discourage aspiration
c. Burp frequently because more air is swallowed which can cause regurgitation/vomiting
d. NGT feeding as ordered
▪ Protrusion of intraabdominal contents into the base of umbilicus which is covered by a translucent sac
(peritoneum without skin)→rupture→evisceration
▪ Herniated organs
OMPHALOCELE
Type of cleft lip: extends into the base of the nose and even the gums in which upper teeth are set may also be deformed
Complete
Characteristics of cleft lip
Associated with deformed dental structures
NURSING DIAGNOSIS
Preoperative of CL/CP
- High risk for aspiration (breastmilk, formula or mucus) related to anatomic defect
- High risk for aspiration (breastmilk, formula or mucus) related to anatomic defect
stomach capacity of 3 months
150-200 ml
intestines which include stomach and liver covered by psa
Herniated organs
NURSING CARE of omphalocele
- Protect sac from trauma and infection
- Prepare the infant for surgery
stomach capacity of 2 years
500 ml
Type of EA/TEF: most common
EA with distal TEF
stomach capacity of 1 month
90-150 ml
Pre-op nursing care for EA/TEF
- Maintain open airway
- NPO
- Administer IVF as ordered
- Oxygen to relieve respiratory distress
Other defects associated with cleft lip/palate
omphalocele, TEF
3Cs of TEF
choking, coughing, cyanosis
purposes of cheiloplasty
- early repair avoids oral deprivation, prevents trauma and difficulty for the parents
- its difficult to bond with an infant with deformed face
- Help infant experience the pleasure in sucking
Palliative surgery for EA/TEF:
* Provision of constant drainage of the esophageal
pouch=tube in the mouth to upper pouch
o Esophageal replacement
Esophagostomy