Dr. Pestana's Notes--Peds, Cardiothoracic, Vascular Flashcards
____ shows up with excessive salivation noted shortly after birth, or choking spells when first feeding. There may even be failure to pass an NG tube
Esophageal atresia
MC type of esophageal atresia. Dx
blind pouch in upper esophagus and fistula btwn lower esophagus and tracheobronchial tree (normal gas in bowel); failure of NG tube + CXR
How do you rule out VACERL anomalies?
vertebral/radial–check xray; imperforate anus–physical, xray; cardiac anomalies–EKG; esophageal atresia–NG tube; renal–US
Tx esophageal atresia
sx–but if delayed, a gastrostomy must be done to protect lungs from acid reflux
For an imperforate anus, look at the anus itself or a ______ nearby. Repair can sometimes be delayed, but must be done before _______.
fistula (vagina or perineum); toilet training time
If imperforate anal surgery needs to be done right away, a ____ is done for high rectal pouches, and later the primary repair; OR a primary repair can be done right away only if _______
colostomy; anal pouch is very close to rectum
Level of pouch of imperforate anus is assessed with a ___ taken ____
xray; upside down (gas goes up w/ metal marker taped to anus)
Congenital diaphragmatic hernia is always on the ___ side of the body. The major issue is _____ that still have fetal-type circulation; if this is the case, the surgery must be delayed _____ in order for maturation to occur
left; hypoplastic lungs; 3-4 days
Tx for babies in respiratory distress; dx
endotracheal intubation, low-pressure ventilation, sedation, NG suction [difficult cases may require extracorporeal membrane oxygenation (ECMO)]; sonogram before birth
In gastroschisis, the umbilical cord is ____ and the bowel is ______.
normal (defect to the right of the cord); angry/matted
In omphalocele, the umbilical cord goes ____ and the bowel is ______.
into the defect (has a thin membrane over bowel); normal
Small defects in the ventral wall can be closed primarily, but large ones require construction of a ______ in order to house and protect the bowel. Complete closure can usually be done in about ____.
Silastic (aka “silo”); one week
Babies with gastrochisis need ______ because the bowel will not work for about 1 month.
vascular access for parenteral nutrition
Exstrophy of the urinary bladder must be repaired within the first ______ of life.
one or two days
Three scenarios that green emesis + “double bubble” on CXR are seen in newborns
(1) duodenal atresia (2) annular pancreas (3) malrotation
What is a harbinger to malrotation besides bilious emesis and CXR finding of a “double bubble” in an infant? Dx?
little normal gas pattern beyond the double bubble on CXR; contrast enema or upper GI study
Clinical signs of malrotation can show up in infants in the first _____ of life.
few weeks
Intestinal atresia is identified in infants w/ green vomiting and multiple _____ throughout the abdomen.
air-fluid levels
No other congenital malformations are associated with intestinal atresia because this condition results from a _______ in utero.
vascular accident
_____ is seen in _____ infants when the first feeding causes intolerance, abd distention and a rapidly dropping platelet count (sign of sepsis).
Necrotizing enterocolitis; premature
Surgical intervention is needed for infants w/ necrotizing enterocolitis in the following scenarios (4)
abd wall erythema, air in portal vein, intestinal pneumatosis, pneumoperitoneum
Meconium ileus is seen in babies w/ _____. Xrays show dialated loops of small bowel and a _____ appearance in the lower abdomen.
CF; ground-glass
_____ enema is both diagnostic (microcolon) and therapeutic (dissolves pellets of meconium) in meconium ileus.
Gastrografin
Hypertrophic pyloric stenosis shows up at age _____, is more common in _____ w/ nonbilious projectile vomiting after each feeding.
3 weeks; firstborn boys
Visible gastric peristaltic waves and a _____ mass in the RUQ is indicative of hypertrophic pyloric stenosis. A ____ can be diagnostic.
palpable “olive-size”; US
Tx of hypertrophic pyloric stenosis in babies
rehydration (correct hypochloremic, hypokalemic metabolic alkalosis), Ramstedt pyloromyotomy or balloon dilation
Biliary atresia should be suspected in infants ______ old who have progressively increasing jaundice. Dx.
6 to 8 weeks; HIDA scan after 1wk phenobarbital
Tx and prognosis of biliary atresia in infants
biliary surgery; 1/3 long-lasting, 1/3 needs liver transplant post-sx, 1/3 need transplant immediately
Hirschprung disease, aka _____, is recognized with chronic constipation. Physical exam.
aganglionic megacolon; rectal exam leading to explosive expulsion of stool/flatus w/ relief of adb distension
Dx Hirschprung dz
Xray can show distended prox colon and “normal” distal colon; confirmation w/ full-thickness bx of rectal mucosa
Intussusception is seen in _____ kids who have episodes of colicky abd pain that makes them double-up and squat.
6 to 12mo-old chubby, healthy-looking
Physical exam of intussuception shows a vague mass on the ___ side of the abd, and “empty” lower quadrant and _____ stools.
right; “currant-jelly”
Dx/therapeutic for Intussusception; last resort tx
barium or air enema; sx
Classic presentations of child abuse
subdural hematoma w/ retinal hemorrhages (shaken), multiple fractures in different bones at dif stages of healing, scalding burns, burns of buttocks
MCC lower GI bleeding in pediatrics. Dx
Meckel diverticulum; radioisotope scan looking for gastric mucosa [remember rule of 2’s]
Tx of undescended testicle.
orchiopexy
What is the term for a testicle that is in the canal at birth but can be easily pulled down where it belongs [NOT undescended testicle]? This is benign.
overactive cremasteric muscle
If an abd mass is found in a child that moves up and down with respiration, it is most likely a _______.
malignant liver tumor (hepatoblastoma or HCC)