DISORDERS OF PRIMARY HEMOSTASIS

Question 1

occurs when small blood vessels leak blood under the skin

Answer 1

PURPURA

Question 2

measure 4-10mm in diameter

Answer 2

PURPURA

Question 3

purpura spots are less than 4 mm in diameter, they are called

Answer 3

PETECHIAE

Question 4

measures less than 2mm

Answer 4

petechiae

Question 5

Pinpoint non-blanching spots

Answer 5

petechiae

Question 6

small bruise cause by blood leaking from broken blood vessels into the tissues of the skin or mucous membranes

Answer 6

Ecchymosis (Raccoon eyes)

Question 7

excessive bleeding that requires medical or physical intervention

Answer 7

Hemorrhage

Question 8

recurrent, chronic bruising in multiple locations

Answer 8

purpura

Question 9

Disorders of vessels and their supporting tissues.

Answer 9

Vascular Disorders

Question 10

Diagnosis is often based on medical history and is made by ruling out other sources of bleeding disorders.

Answer 10

Vascular Disorders

Question 11

Vascular malformation involves vessels throughout the body, which are dilated and disorganised. It is characterised by the presence of widespread telangiectatic lesions of the skin and mucous membrane

Answer 11

Hereditary Hemorrhagic Telangiectasia (Rendu-Osler-Weber Syndrome)

Question 12

Lesions develop on the tongue, lips,
palate, face, and hands.

Answer 12

Hereditary Hemorrhagic Telangiectasia (Rendu-Osler-Weber Syndrome)

Question 13

Tumor of the vessel

Answer 13

Hemangioma-Thrombocytopenia Syndrome (kasabach merrit syndrome)

Question 14

Bleeding diathesis

Answer 14

Petechiae
Purpura

Question 15

malformations include

Answer 15

Giant cavernous hemangioma

Question 16

Giant cavernous hemangioma

Answer 16

tumor in the blood vessel

Question 17

More severe than Eccymosis

Answer 17

hematoma

Question 18

caused by a broken blood vessel that was damaged by surgery or an injury.

Answer 18

hematoma

Question 19

More severe than Eccymosis

Answer 19

hematoma

Question 20

autosomal dominant disorder characterized by hyperdistensible joints and fragile skin

Answer 20

ehlers-danlos syndrome/cutis hyperelastica

Question 21

autosomal dominant genetic disorder due to mutation of the gene

Answer 21

marfan

Question 22

resulting in abnormalities in connective tissues and risk for bleeding and bruising

Answer 22

MARFAN SYDROME

Question 23

autosomal dominant genetic disorder due to mutation of the gene (FBN1) resulting in abnormalities in connective tissues and risk for bleeding and bruising

Answer 23

MARFAN SYNDROME

Question 24

An autosomal recessive disorder affecting elastic fiber of connective tissue of skin and arteries

Answer 24

Pseudoxanthoma Elasticum / Gröenblad-Strandberg

Question 25

rare autosomal dominant disorder

Answer 25

osteogenesis imperfecta

Question 26

known as simple purpura or devil’s pinches result of skin fragility

Answer 26

primary purpura

Question 27

seen in older individuals or in individuals undergoing corticosteroid therapy; purpuric lesions occur on the hand and arms.

Answer 27

senile purpura