Dev Anomalies

Question 1

Histo difference of Fordyce granules vs normal sebaceous gland.

Answer 1

• increase no. Of lobules and ducts >keratin plugging ducts

Not associated with hair follicle

Question 2

Appearance of hecks disease, single and cluster?

Answer 2

Single:broad base> slight elevate, papillary
Cluster: small, closely knitted,cobblestone

Question 3

Main histo of hecks disease

Types if cells seen

Answer 3

Acanthosis of spinous cell layer

Koilocytes, vacoulated, pyknotic nucleus

Question 4

Leukoedema appearance

Histo, epi, conn, suoerficial

Answer 4

Early: fillmy opalescence 
Final: grey white wrinkled
Epi: edematous spinous, 
Thick irregular rete ridges
Superficial: parakeratotic

Question 5

Part affected in facial hemiatrophy?

Change in eyes and nerves

Answer 5

Skin- soft tissue,sc tissue, bone nerve carti
Enophtahlmous,
Trigeminal neuralgia, contralateral Jacksonian epilepsy

Question 6

Dd of facial hemiatrophy

Answer 6

Fgh
Fat atrophy
Goldenhar syndrome
Hemifacial microsomia

Question 7

Coupe de sabre is seen in?

Also called

Answer 7

Facial hemiatrophy

Parry rhomberg

Question 8

How is facial hemihypertrophy seen?

Bone? Tongue, mucosa? Teeeth

Answer 8

Only face,with limbs or whole half body
Wide thick
Macroglossia, lingual papillae 
Increase in mass, pendulous folds
Increase size no. Affects dentition

Question 9

Dd of FHH

Ass with

Answer 9

Neurofibromatosis
Fibrous dysplasia

Beckwith widemann
Mc cune albright

Question 10

In macrognathia of maxillae> leontiasis ossea, in mandible prognathism
Feats of prognaths

Answer 10

Glenoid,anterior
Ramus: large
Angle:steep
Maxilla: decrease in size.

Question 11

When is mouth breathing seen?
Cause of agnathia
Feat of agnathia, ear

Answer 11

In micrognathja of maxillae
No migration of NCC
Otocephaly

Question 12

Vander woude syndrome is caused by deletion of?
Manifests?
Extra oral manifests of it?

Answer 12

1q32
Cleft palate> isolated cleft lip, missing teeth esp maxillary hypodontia
Leg: popliteal webs, limb abnormalities,
Brain: abnormal
Hirschprung disease
Accessory nipples.

Question 13

Histo? Epi OF MRG,rete ridge?

Answer 13

Pseudoepitheliomatous hyperplasia

Keratin pearls in rete ridges

Question 14

Common teeth of microdontia?

Answer 14

Max li, M3

Question 15

Criteria for concrescence

Answer 15

Proximation of adjacent teeth

And depo of cementum due to chronic inflammation, periodontal disease

Question 16

Dilapidation mecha

Ass with

Answer 16

Trauma> due to disturbance in unminerakized and mineralised part of tooth
@S AX I ED
Smith magenis syndrome
Axenfield rieger syndrome 
Ehler danlos 
Congenital ichthyosis

Question 17

Rubinstein Taybi?

Main compli

Answer 17

Talons cusp

Dev groove>

Question 18

Etio of dens in dente

Pathog

Answer 18

Focal failure of IEE

Rapid aggressive prolif of IEE invading dental papilla

Question 19

Leongs premolar?

Patho?

Answer 19

Dens evaginatus @ lwang jasto enamel pearl pm ma

Prolif of certain area of IEE

Question 20

Enamel pearl,why?

Tt?

Answer 20

Intact HERS> malassez > change to ameloblasts

Enameloplasty too.