cystic fibrosis Flashcards
1
Q
what is CF
A
genetic disorder affecting lungs, pancreas, liver, intestine, reproductive organs
viscous sputum, chest infections, malabsorption
2
Q
treatment
A
prevent lung infections and maintain lung function
mucolytics - dornase alfa
- aids to clear mucus/sputum from lungs
long term antibacterial considered to suppress chronic staph aureus
nutrition and exocrine pancreatic insufficiency - pancreatin
monitor pts for liver disease, diabetes and bone density