cutan syste

Question 1

Systemic

– Primary—– Myeloma-associated• Macroglossia, purpura, carpal tunnel

Answer 1

AL

Question 2

β-microglobulin

Answer 2

– Muckle-Wells

Question 3

– FMF-—–

Answer 3

AA

Question 4

Transthyretin

Answer 4

Hemodiaylsis

Question 5

Macroglossia, purpura, carpal tunnel

Answer 5

Myeloma-associated•

Question 6

– Secondary——•

Answer 6

AA

Question 7

Keratinocyte tonofilament

-Keratinocyte tonofilament

Answer 7

Macular/lichenoid-• BCC or SCC

Question 8

of PAN patients may be HCV +

Answer 8

– 12-31%

Question 9

• Adenomas, goiter, duct cyst and follicular type of CA

Answer 9

Cowden’s syndrome

Question 10

• Macular amyloidosis and men

* Zollinger-Ellison syndrome, medullary thyroid carcinoma, pheochromocytoma, and parathyroid neoplasia

Answer 10

Type IIa

Question 11

• Multiple mucosal neuromas
• Marfanoid habitus, Hirschsprung disease, medulloblastoma, medullary thyroid carcinoma, pheochromocytoma and ocular neuromas

Answer 11

– Type IIb/III

Question 12

Facial angiofibromas, collagenomas, lipomas, hypopigmented macules and café-au-lait macules
• PUD (as part of Zollinger-Ellison syndrome), parathyroid hyperplasia or adenoma, pancreatic tumors and pituitary neoplasia

Answer 12

– Type I

Question 13

medullary thyroid carcinoma pheochromocytoma

Answer 13

Type IIb/III

Type IIa

Question 14

HLA class DH

Answer 14

HLA class II DQ2 genotype

Question 15

Dapsone ?DH

bowel disease

Answer 15

does not help