Congenital Heart Defects

Question 1

Fixed S2 Split
Associated with Down Syndrome
Right Atrial/Ventricular Enlargement

Answer 1

Atrial Septal Defect

Non-Cyanotic

Question 2

Harsh Holosystolic Murmur on Left Sternal Border

Associated with Fetal Alcohol Syndrome

Sx’s of CHF: Frequenct UR Infection, Tachypnea, Poor Feeding

Answer 2

Ventricular Septal Defect

Non-Cyanotic

Question 3

Risk Factor: Rubella
Continuous Machine Like Murmur
Left Sided Enlargement

Answer 3

Patent Ductus Arteriosus (PDA)

Non-Cyanotic

Question 4

LVH
Paradoxical Splitting
Weak Pulses, Syncope, Angina, Dyspnea

Answer 4

Aortic Stenosis

Non-Cyanotic

Question 5

Prominent A Wave
Murmur at Left 2nd intercostal
RVH

Answer 5

Pulmonic Stenosis

Non-Cyanotic

Question 6

Associated with Turner Syndrome

LVH
Notching on Ribs

HTN

Answer 6

Coarctation of Aorta

Non-Cyanotic

Question 7

Boot Shaped Heart

Squatting releaves cyanosis

Answer 7

Tetralogy of Fallot

Question 8

Mechanism and 4 Abnormalities of

Tetralogy of Fallot

Answer 8

1) Pulmonic Stenosis
2) Right Ventricular Hypertrophy (boot shape)
3) Over-riding Aorta
4) Ventricular Septal Defect (R -> L Shunt)

Question 9

Treatment for Transposition of Great Arteries

Answer 9

PGE to maintain PDA
Arterial Switching (must also switch coronary arteries)