Congenital Heart Defects Flashcards

1
Q

What is the most apparent signs in paediatric congestive heart failure?

A

Hepatomegaly
Cyanosis
Murmors

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
2
Q

What are the 3 main ways congenital heart defects present?

A

Heart Failure

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
3
Q

Whats are the symptoms of heart failure in an infant?

A

Feeding difficulties (sweating)
Tachyponea
Faltering Growth
Marked oedema (sacral)

Hepatomegaly / Cyanosis / Murmors

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
4
Q

Whats are the symptoms of heart failure in an toddler?

A

Reduced appetite
Reduced activities

Hepatomegaly / Cyanosis / Murmors

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
5
Q

Whats are the symptoms of heart failure in an Older Children?

A
Exercise intolerance / Fatigue 
Hepatomegaly 
Orthopnea 
Oedema  
Abdominal Pain

Hepatomegaly / Cyanosis / Murmors

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
6
Q

What is the most common heart defects found in downs?

A

Septal (50% of downs have a cardiac issue)

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
7
Q

What are the murmur found in downs heart defects? (3)

A

Ventricular septal = Pan-systolic
Atrial septal = Ejection systolic

Atrio-ventricular = Pan-systolic

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
8
Q

Why is a ventricular septal defect pan-systolic?

A

Blood goes straight from ventricle to ventricle
(mostly from left to right)
No valves to overcome so all over systole

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
9
Q

Why is a Atrial septal defect Ejection systolic?

A

Blood does not go through the valve = Flow murmur from right ventricle systole

Blood flows into right atria from both left atria & vena cave = more blood than normal
= More blood entering the right ventricle
= More blood exiting during systole

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
10
Q

Why is a Atrio-ventricular septal defect pan-systolic?

A

The ventricular septal defect dominates

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
11
Q

What is the murmur in patent ductus arteriosus?

A

‘Machine like’ constant mummer

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
12
Q

Why is the murmur in patent ductus arteriosus constant?

A

Aortic arch & pulmonary trunk are linked and due to the constant changes of pressure in the cardiac system blood will constantly be flowing through the ductus creating background noise.

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
13
Q

What murmurs are pathological in children? (3)

A

Diastolic mummers
Murmurs which change with positioning
Murmurs which can be heard across the heart

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
14
Q

What is another name for DeGeorge syndrome?

A

22q11.2 deletion

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
15
Q

What cardiac abnormalities can be present in DeGeorge?

A

Truncus/Ductus arteriosis

Ventricular septal defects

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
16
Q

What are other non-cardiac features of DeGeorge?

A

CATCH-22

C-ardiac issues
A-bnormal face
T-hymic aplasia (only give radiated blood)
C-left palate
H-ypoparathyriodism (monitor calcium) 
22-q11.2 deletion
How well did you know this?
1
Not at all
2
3
4
5
Perfectly
17
Q

What is the main common congenital heart defects in Downs (T21)?

A

Atrio-ventricalar septal defects

18
Q

What is the main common congenital heart defects in Edwards (T18)?

A

Atrio-septal defects

19
Q

What is the main common congenital heart defects in DeGeorge (22q11.2)?

A

Interrupted aortic arch (often truncus) +/- Ventricular septal defec

20
Q

What is the main common congenital heart defects in Turners (45XO)?

A

Bicuspid aortic valve

21
Q

What is the main common congenital heart defects in Prolonged QT?

A

Ventricular dysrithmia

22
Q

What are the most common causes of Patent Ductus Arteiosis?

A

Premature Birth
Rubella infection during pregnancy
Being Female
DeGeorge (22q11.2)

23
Q

What causes Epstine’s abnormality?

A

Lithium during birth

24
Q

What is Epstine’s abnormality?

A

Abnormally small right ventricle
Floppy Tricuspid valve
Atrioseptal defect

All leading to a dilated right atrium

25
Q

What is the murmur heard in Epstines abnormality?

A

Low systolic mummer over tricuspid valve

26
Q

What are the symptoms of foetal alcohol syndrome?

A

Smooth philtrum & small lip

Ventricular septal defects (pan-systolic)

27
Q

What congenital heart defect are babies with diabetic mothers more likely to develop?

A

Translocation of the great arteries (aorta from RV and pulmonary trunk from LV)

Presents early
Unchanged O2 sats from high flow O2

28
Q

What congenital heart defect are babies with Rubella mothers more likely to develop?

A

Patent ductus artiosis

29
Q

What congenital heart defect are babies with Lupus mothers more likely to develop?

A

Complete Heart Block

30
Q

What is Hydrops Fetalis?

A

Accumulation of fluid within featal compartments (plural or pericardial effusions)

31
Q

What increases the risk of Hydrops Fetalis?

A

Maternal viral infections (CMV / Rubella / PV-B19)
Pre-Eclamsia
Iron deficiency
Polyhydramnios

32
Q

What medication should NEVER be given in Translocation of the great arteries TGA

A

Ibuprofen

Inhibits prostoglandin synthesis

Prostoglanins are used to keep the ductus arteriosis open (acts as a shunt)

Atrial & Ventricle Defects help shunt too

33
Q

What is a dangerous side effect of Prostaglandin E?

A

Increases temperature = danger of missing sepsis

34
Q

What is computation of the aorta?

A

Narrowing of the Aorta

35
Q

How does computation of the aorta cause cerebral aneurysms?

A

Blood pressure increases due to Low blood pressure in the kidneys receptors
= Increase in Blood pressure in the upper body (before the stenosis)

36
Q

What clinical sign can be used to identify computation of the aorta?

A

Weak femoral pulses vs carotid/brachial pulses

37
Q

What is the treatment of computation of the aorta?

A

Angioplasty +/- stent

38
Q

What are the structural changes in Tetralogy of Fallot?

A

Right Ventricular Hypertrophy
Overriding Aorta
Right ventricular outflow obstruction
Large ventricular septal defect

39
Q

What is the RSV prophylaxis used in babies with congenital heart defects?

A

Palivizumab

40
Q

What does the Respiratory syncytial virus cause?

A

Bronchiolitis