Congenital Heart

Question 1

4 types of ASDs

Answer 1

1. Primum
2. Secundum
3. Sinus Venosus
4. Coronary Sinus

Question 2

Which ASD is associated with Trisomy 21?

Answer 2

Ostium Primum

Question 3

A Primum ASD + Inlet VSD = ?

Answer 3

Complete Atrioventricular Canal (CAVC)

Question 4

Which ASD is associated with cleft anterior mitral leaflet?

Answer 4

Ostium Primum

Question 5

Which ASD is associated with cleft septal tricuspid valve leaflet?

Answer 5

Ostium Primum

Question 6

Which ASD is associated with Mitral Valve Prolapse?

Answer 6

Ostium Secundum

Question 7

This ASD is a defect in the septum primum located in the fossa ovalis

Answer 7

Ostium Secundum ASD

Question 8

This ASD is associated with anomalous pulmonary venous return

Answer 8

Sinus Venosus ASD

Question 9

This ASD is associated with persistent left superoir vena cava

Answer 9

Coronary Sinus ASD

Question 10

Outlet VSD is Type ____

Answer 10

Type 1

Question 11

Membranous VSD is Type ____

Answer 11

Type 2

Question 12

Inlet VSD = AV canal type is Type ____

Answer 12

Type 3

Question 13

Muscular VSD = Trabecular VSD is Type ____

Answer 13

Type 4

Question 14

The most common type of VSD in adults is Type ____

Answer 14

Type 2 = Membranous

Question 15

In the RV inflow/outflow view, this VSD is closer to the Pulmonic Valve than the tricuspid valve

Answer 15

Type 1 = Outlet VSD

Question 16

This VSD is associated with intraventricular aneurysms

Answer 16

Type 2 = Membranous VSD

Question 17

In the RV inflow/outflow view, this VSD is closer to the Tricuspid Valve than the pulmonic valve

Answer 17

Type 2 = Membranous VSD

Question 18

Type of VSD in Tetralogy of Fallot

Answer 18

Type 2 = Membranous VSD = Anterior malalignment VSD

Question 19

What are the “4” components of Tetralogy of Fallot

Answer 19

1. VSD
2. Overriding Aorta
3. Pulmonic Stenosis
4. RVH

Question 20

This VSD is associated with Trisomy 21

Answer 20

Type 3 = Inlet VSD

Question 21

Primum ASD + ___________ = CAVC

Answer 21

Inlet VSD

Question 22

A defect in the muscular Ventricular septum is a _________ VSD

Answer 22

Trabecular = Muscular = Type 4 VSD

Question 23

Right aortic arch occurs in about ____% of Tetralogy of Fallot

Answer 23

25% have right aortic arch

Question 24

Pentalogy of Fallot is Tetralogy PLUS _______

Answer 24

Atrial septal Defect (occurs in about 10%) of Tetralogy

Question 25

___________ Syndrome is associated with supravalvular aortic stenosis

Answer 25

William’s Syndrome

Question 26

Williams syndrome is due to what gene deletion on chromosome 7?

Answer 26

Elastin Gene on Chromosome 7

Question 27

Williams syndrome leads to arteropathy and narrowing at the ____ _____ ____

Answer 27

Sino-tubular Junction

Question 28

A complete AV Canal is formed by an inlet VSD + _______________

Answer 28

A primum ASD

Question 29

Supravalvular Aortic stenosis and sudden death (Williams’s/ Barlow’s/ Turner/ Shone/ Noonan)

Answer 29

Williams syndrome

Question 30

Bileaflet mitral prolapse and myxomatous mitral valve
(Williams’s/ Barlow’s/ Turner/ Shone/ Noonan)

Answer 30

Barlow’s disease

Question 31

Coarctation of the aorta, bicuspid AV, AS, Hypoplastic left heart (Williams’s/ Barlow’s/ Turner/ Shone/ Noonan)

Answer 31

Turner’s syndrome

Question 32

Left sided obstruction, parachute mitral valve, supramitral ring, subaortic stenosis and aortic coarctation
(Williams’s/ Barlow’s/ Turner/ Shone/ Noonan)

Answer 32

Shone Complex

Question 33

Associated with isolated pulmonic stenosis
(Williams’s/ Barlow’s/ Turner/ Shone/ Noonan)

Answer 33

Noonan Syndrome