Congenital Duodenal Obstruction Flashcards
Congenital duodenal atresia is a congenital bowel obstruction, usually affecting what part of duodenum.
second part
three types of congenital duodenal obstruction are
.
Congenital duodenal obstruction is also classified into:
− Complete: caused by duodenal atresia or complete duodenal diaphragm
− Incomplete (Partial): caused by duodenal stenosis, duodenal diaphragm with a central hole, or extrinsic causes.
Extrinsic causes are annular pancreas , Ladd’s bands, duplication cyst, portal vein passing anterior to duodenum, etc.
Presentation
recognized antenatally by the classic double bubble appearance on ultrasound and associated maternal polyhydramnios (30–65 % of cases).
Early onset of bilious vomiting and feeding intolerance
Features of trisomy 21 (Down’s syndrome).
Examination
- Upper abdominal distension or scaphoid abdomen in atresia if the stomach is empty or the child is on nasogastric drainage.
- Bilious aspirate in the nasogastric tube.
dehydration, and associated cardiac malformation.
Associated Anomalies of congenital duodenal obstruction
Trisomy 21 (Down’s syndrome) → 28.2 %
- Congenital heart disease → 22.6 %
- Annular pancreas → 23.1 %
- Intestinal malrotation → 19.7 %
- Esophageal atresia/tracheoesophageal fistula
Most common Associated Anomalies of congenital duodenal obstruction is
Down syndrome
Diagnosis of congenital duodenal obstruction includes
A plain abdominal X-ray showing double bubble confirm the diagnosis of complete duodenal obstruction
Contrast study
The presence of a duodenal diaphragm with a central aperture is confirmed by the incomplete duodenal obstruction in absence of malrotation ( small distal bowel gas and thin contrast seen distally )
Treatment
Gastric decompression is essential to prevent aspiration
Fluid resuscitation
Open surgery or laparoscopic correction of congenital duodenal obstruction can be performed.
- A diamond-shaped duodeno-duodenostomy (as described by Kimura) or a simple duodenoduodenostomy is performed in cases of type 2 atresia and with annular pancreas.
side-to-side duodeno-jejunostomy in type 3 atresia with a wide gap or if the atresia is in the third or fourth parts of duodenum
Postoperative Care
- All infants are maintained on bowel rest and parenteral nutrition.
- Nasogastric aspirates are monitored and fluid losses are replaced
Complications of the surgery
Anastomotic leak.
- Wound infection.
- Delayed gastric emptying with consequent delayed feeding