Congenital Flashcards
What is SINUS OF VALSALVA ANUERYSM?
aneurysm of one of the sinus’, appears as a thin dilated area that projects into adjacent cardiac structures often with a fistula
Draw out what a SINUS OF VALSALVA ANEURYSM would look like & in the view you would see it in
PSSAX AV
NCC - into RA
LCC - into LA
RCC - into RV
What is a CORONARY AV FISTULA?
rare congenital anomaly where there is an abnormal communication from coronary artery to coronary sinus
When does a CORONARY AV FISTULA present?
in young adults as continuous murmur
What is seen on ECHO of a CORONARY AV FISTULA?
- receiving vessel/chamber & proximal coronary artery may be dilated
- may see echolucent entro site
- may see abnormal color flow into vessel/chamber
- may see disturbed color flow in fistula
What is EBSTEIN ANOMALY?
one (usually septal) or more of the TV leaflets are adhered to RV endocardium
Draw out what EBSTEIN ANOMALY would look like
Define LEVOCARDIA
apex towards left
Define DEXTROCARDIA
apex towards right
Define SITUS SOLITUS
normal position of thoracic and abdm organs
Define SITUS INVERSUS
organs of chest and abdm are arranged in a perfect mirror image reversal of the normal position
Define & Draw out NORMAL POSITION SITUS SOLITUS
normal position of thoracic and abdm organs with apex to left
Define & Draw out SITUS INVERSUS WITH DEXTROCARDIA
organs of chest and abdm switched with apex to right
Define & Draw out SITUS SOLITUS WITH DEXTROCARDIA
normal position of thoracic and abdm organs BUT apex to right
Define & Draw out SITUS INVERSUS WITH LEVOCARDIA
organs of chest & abdm switched BUT apex to left
what is the FIRST and SECOND most common congenital defect in adults?
- bicuspid AV
- ASD
What are the types of ASDS?
- secundum
- primum
- sinus venosus
What is a SECUNDUM ASD and DRAW it out
defect at the central section of IAS at fossa ovalis
Name a type of SECUNDUM
patent foramen ovale
What is a PFO and DRAW it out
lesser form of ASD and it’s failure of the foramen ovale to close
What is a PRIMUM ASD and DRAW it out
ASD inferior to secundum, located near atrioventricular connection
What is a SINUS VENOSUS?
defect at the base of LA, superior and posterior near junction of SVC and RA
A Sinus Venosus may be associated with what?
- PAPVR (partial anomalous pulmonary venous return)
- TAPVR
What is the most common form of ASD and what is it associated with?
-secundum
-MVP
PRIMUM ASD is associated with what abnormalities?
abnormalities of the atrioventricular valves like:
1. AV canal defect
2. cleft (divided) AMVL
What are the ECHO FINDINGS for ASDs?
- color jet across atrial septum into RA
- RAE, RVE,PSM due to increased volumes
- L - R shunt bc LA pressure > RA
- may have IAS aneurysm
- “T” artifact in apical
What are DOPPLER FINDINGS for ASDs?
- PW location, CW velocity, Qp/Qs severity
- low velocity flow; slightly faster in diastole due to pressure
What are the TYPES of VSDs and WHERE are they located?
1.membranous/perimembranous - membranous septum
- muscular/trabecular- any location in the muscular portion of the septum
- inlet - below AV between TV and MV annulus
- supracristal/outlet - RVOT portion of septum
What are the ECHO FINDINGS for VSDs?
- LAE, hyperdynamic LV or LVE due to LV volume overload
- color jet LV to RV
- PISA may be seen on left side of IVS if signif.
What can lead to PHTN in regards to VSDs?
large shunts