Chd Flashcards
Success of fontan procedure for tricuspid atresia depends on
HIGH systemic venous pressure and maintaining both low PVR and low left atrial pressure
For triscuspid atresia failed fontan procedure what may be necessary
Heart transplant
What is Tricuspid atresia surgical management
Fontan procedure
Tricuspid atresia -babies are cyanotic at birth and require “this” to survive
Prostaglandin E1 infusion with or without other palliative procedure
For tricuspid atresia- what is necessary for blood to flow from the left ventricle into the pulmonary circulation
PDA or VSD
Tell me exactly what is the problem with tricuspid atresia
Absence or permanent closure of the tricuspid valve
Tricuspid atresia-what is the left ventricle and right ventricle
Small right ventricle large left ventricle
Tricuspid atresia can have transposition of the great vessels
Dextrotransposition
Nondextransposition
What is the flow of blood for tricuspid atresia
Blood goes from RA- asd or pfo to LA- through mitral valve to vsd- to pulmonary artery
If no VSD- blood flows through pda
Signs of symptoms of tricuspid atresia
Clubbing in older children Tachypnea Prominent a waves Abnormal pulses Hepatic enlargement Heart failure
What is ebstein anomaly
Downward displacement of the valve because of abnormal attachment of valve leaflets
What is the most common type of ASD
Ostium secundum at the level of foremen ovale
What ASD is associated with mitral regurgitation
Located low in atrial septum
What ASD is located high in atrial septum
Sinus venous
What type of shunt is ASD
Left to right shunt b/w the 2 atria
For ASD what can air bubbles lead too
Paradoxical Emboli that can lead to heart attacks and strokes
Treatment of ASD
Early repair is advocated
Banding of pulmonary artery to reduce the magnitude of left to right shunt
What infection can occur with ASD
Recurrent pulmonary infections
What should be avoided in ASD
Increase in SVR-worsen left to right shunting
ASD what is commonly seen post op
Svt and about conduction is common
In ASD what will volatiles and positive pressure ventilation do to shunting
Decrease svr
Ppv will increase pvr and decrease the shunt
What may present post op with VSD
3rd degree heart block may present
What shunt has Recurrent pulmonary infections and CHF are common
VSD left to right
True or false
Small VSD close during childhood spontaneously
True
Large VSD s usually produce large left to right shunts that vary directly with____ and indirectly with___
Directly with SVR
Indirectly with PVR
VSD are mostly a symptomatic what type of murmur do they have
Loud pan systolic murmur along left stern also border
Name the most common VSD
Membranous VSD
Name the 4 types of VSD
Membranous VSD
Muscular VSD
Supra-cristal VSD
Av canal type VSD
For a VSD WHAT DO YOU SEE ON THE CXR
Biventricular hypertrophy
Pul HTN
Transposition of the great arteries must include which holes in the heart for blood to mix
Survival is only possible through mixing of blood through foramen ovale-PDA AND SOMETIMES A VSD
Transposition of the great arteries includes what medication for survival
Prostaglandin E1
What ventricle does transposition of the great vessels effect
Mimics tof- when a VSD and pulmonic stenosis occurs. Obstruction effects the left ventricle NOT the right
Describe total anomalous venous return
Pulmonary veins do not connect to the left atrium. Instead blood returns to the right atrium or prior to the ra- and mixes with the deoxygenated blood
How does the baby survive total anomalous venous return
Blood reaches the left side of the heart via an foramen ovale or an ASD.
For total anomalous venous return - why does venous congestion begin to occur.
Severe pulmonary congestion occurs when the ductus venous begins to close.
How is total anomalous venous return corrected
The pulmonary venous trunk is reanastomosed into the left atrium and the asd is closed
Describe truncus arteriosus
Single arterial trunk supplies the pulmonary and systemic circulation
What accompanies truncus arteriosus
A VSD to allow both ventricles to eject into it
During truncus arteriosus- PVR gradually decreases after birth but pulmonary blood flow increases resulting in what
Heart failure
Patients with cyanotic heart disease have what response to hypoxemia
Blunted response
Patients with cyanotic heart disease have what response to hyper apnea
Normal response
What does methergine do to parturients
Increases svr
What does oxytocin do to parturients
Decreases svr and increases HR and PVR
Normal aortic valve area
2.5-3.5cm
Severe aortic stenosis is when the valve is less than or equal to
1cm2
Hr for AS
60-90
Nsr
Maintain preload, after load, contractility
AS
treatment for bradycardia
Treatment for tachycardia
Atropine
Esmolol
AS when is spinal and epidural tolerated
Mild to moderate stenosis
Epidural is better tolerated
When are spinal and epidurals contraindicated in aortic stenosis
In severe aortic stenosis
In AS- what medication is effective for treating svt and ventricular dysrhythmics
Amiodarone and lidocaine
What medication do we use to treat hypotension in AS
Small doses of neo
Describe coarctation of the aorta
Obstruction located in the descending aorta
Describe preductal coaractation of the aorta
Narrowing occurs proximal to the opening of the ductus- marked differences occur between the lower and upper half of the body-lower half is cyanotic
Coarctation of aorta with or without left ventricular failure=
HTN in upper body with bounding pulses and hypotension of lower extremities with weak or absent pulses
Which cardiomyopathy is genetically transmitted
Hypertrophic cardiomyopathy
The most common cause of sudden death in pediatric and young adult population
Hypertrophic cardiomyopathy
What are the 4 major changes in hypertrophic cardiomyopathy
Ventricular hypertrophy
Decreased ventricular chamber size
Increased ventricular wall thickness
Impaired ventricular relaxation
What is described as the rapid acceleration of blood traveling through a narrow outflow tract
Venturi effect
The presence of “this makes the coronary artery walls narrowed in hypertrophic cardiomyopathy
Collagen
What happens to the left ventricle in hypertrophic cardiomyopathy
Asymmetric hypertrophy of inter ventricular septum of LV CAUSES LEFT OUTLFOW TRACT OBSTRUCTION - hemodynamics consequences are similar to AS