Chapter 5: Pediatric Surgery Flashcards
What are some physical symptoms associated with Esophageal Atresia?
- Excessive salivation noted shortly after birth
2. Choking spells when first feeding is attempted
Where with the NG tube placement be seen on an XRAY with a baby with esophageal atresia?
NGT will be seen coiled in the upper chest when XRAYs are done.
What is the most common type of esophageal atresia?
A blind pouch in the upper esophagus and a fistula between the lower esophagus and the tracheobronchial tree. Normal gas pattern in the bowel.
What is the VACTER constellation that needs to be ruled out before therapy is under taken for esophageal atresia?
- Vertebral
- Anal: Imperforation **
- Cardiac
- Tracheal
- Esophageal
- Renal
- Radial
If surgery has to be delayed in esophageal atresia what has to be done?
A gastrostomy has to be done to protect the lungs from acid reflux.
What VACTER constellation should you be wary of on physical exam, that if its there you should look for the others?
Imperforate Anus.
What should you look for if you have an imperforate anus?
Look for a fistula nearby to vagina or perineum
If a fistula is present with an imperforate anus what should you do surgically
Repair can be delayed until further growth (but before toilet training time)
If there is no fistula present with an imperforate anus what should you do surgically?
A colostomy needs to be done for high rectal pouches (and later the repair) or a primary repair can be done right away if the blind pouch is almost at the anus
How is the level of the pouch for an imperforate anus determined?
With X-rays taken upside down so that the gas in the pouch goes up , with a metal marker taped to the anus
In a congenital diaphragmatic hernia what side do they happen on?
Always on the left and the bowel will be up in the chest.
What is the problem with a congenital diaphragmatic hernia?
the hypo plastic lung that still has fetal type circulation
How long do you have to wait to repair a congenital diaphragmatic hernia?
3-4 days to allow maturation.
What do babies need if they have a congenital diaphragmatic hernia?
- respiratory distress and need endotrachaeal intubation
- low pressure ventilation (careful not to blow up the other lung)
- sedation
- NG suction
In a difficult case of congenital diaphragmatic hernia what might the baby need?
Extracoporeal membrane oxygenation (ECMO)
How are patients diagnosed with a congenital diaphragmatic hernia?
before birth by sonogram
What are the two abdominal wall defects in the middle of the belly?
- Gastroschisis
2. Omphalocele
In gastroschisis where is the defect in relation to the cord? is the defect protected?
The cord is normal (it reaches the baby) and the defect is to the right of the cord.
The cord has no protective membrane and the bowel looks angry and matted.
In an omphalocele where does the cord go?
The cord goes to the defect, which has a thin membrane under which one can see normal-looking bowel and a little slice of liver
How are large defects in an omphalocele reduced?
By the construction of a Silastic “silo” to house and protect the bowel. The contents are then squeezed into the belly, a little bit every day until complete closure can be done in about a week
What other important thing do babies with gastroschisis need because of the angry looking bowel?
Vascular access for parental nutrition. the bowel will not work for about 1 month.
Describe the appearance of exstrophy of the urinary bladder.
Another abdominal wall defect but over the pubis (which is not fused), with a medallion of red bladder mucosa, wet and shining with urine.
How quickly do you need to fix exstrophy of the urinary bladder?
Repair must be done within the first 1 or 2 days of life. delayed repairs do not work.
What is a double bubble sign on x ray?
A large air-fluid level in the stomach, and a smaller one to its right in the first portion of the duodenum.