Cardiomyopathies

Question 1

Types of cardiomyopathy and their possible presentations

Answer 1

Acquired
Inherited

Can present in a variety of ways
Dilated - stiff tissue => difficulty contracting
Hypertrophic - difficulty relaxing
Arrythmogenic - conduction and electrical issues => arrythmias

Question 2

HOCM

• pathophysiology
• presentation
• findings on diagnosis
• management

Answer 2

AD - most common cause of SCD in young
-diastolic dysfunction => low CO

~~~
Asymptomatic
If symptomatic
-SOBOE, chest pain
-syncope post-exercise
Can lead to ventricular arrythmia, HF => SCD

Echo
Ejection systolic murmurs - MR
-increases with Valsalva
-decreases with squats
SAM of ant mitral valve leaflet
Asymmetric hypertrophy

Amiodarone
Bb/verapamil for symptoms
Cardioverter defib
Dual chamber pacemaker
Endocarditis prophylaxis

Drugs to avoid
-nitrates
-ACEi
-inotropes

Question 3

Dilated cardiomyopathy

• pathophysiology
• presentation
• findings on diagnosis

Answer 3

Most common cardiomyopathy
-difficulties contracting

HF findings
Systolic murmur => regurg
Ballooning on CXR

Question 4

Arrythmogenic right ventricular cardiomyopathy

• pathophysiology
• presentation
• management

Answer 4

AD

Palpitations
Syncope
SCD

Soltalol
Catheter ablation => prevent VT
ICD