Carbohydrates

Question 1

Synthesis of UDP-Glucose

Answer 1

Phosphoglucomutase; UDP-Glucose Pyrophosphorylase

Question 2

Glycogen Branching

Answer 2

Amylo-Alpha(1,4)-Alpha(1,6)-transglucosidase

Question 3

Co-enzyme: Glycogen Phosphorylase

Answer 3

Pyridoxal Phosphate

Question 4

Glycogen debranching enzymes

Answer 4

Alpha (1,4)-Alpha (1,4)-Glucantransferase; Amylo-Alpha (1,6)-Glucosidase

Question 5

G1P > G6P > Glucose

Answer 5

Phosphoglucomutase; Glucose-6-Phosphatase

Question 6

Galactose > Galactose-1-Phosphate

Answer 6

Galactokinase

Question 7

G1P > UDP Galactose; Classic Galactosemia

Answer 7

Galactose-1-Phosphate Uridyl Transferase (GALT)

Question 8

UDP-Galactose > UDP-Glucose

Answer 8

UDP-Hexose-4-Epimerase

Question 9

Fructose > Fructose-1-Phosphate; Essential Fructosuria

Answer 9

Fructokinase (alt: Hexokinase)

Question 10

Fructose-1-Phosphate > DHAP + Glyceraldehyde; Hereditary Fructose Intolerance

Answer 10

Aldolase B

Question 11

Glucose > Sorbitol

Answer 11

Aldose Reductase

Question 12

Sorbitol > Fructose

Answer 12

Sorbitol Dehydrogenase

Question 13

Ascorbic Acid Synthesis

Answer 13

L-Gulonolactone Oxidase

Question 14

Essential Pentosuria

Answer 14

Xylulose Reductase

Question 15

UDP-Glucose > UDP-Glucoronic Acid

Answer 15

UDP-Glucose Dehydrogenase

Question 16

Cofactor: Transketolase (PPP)

Answer 16

Thiamine