Browns syndrome Flashcards

1
Q

what are features of browns syndrome

A

restriction of elevation in adduction

normal or near elevation in abduction

postive force duction test

absence of muscle sequelae expect overaction of the contralateral synergist

downdraft adduction

widening of palpebral fissure on adduction

v pattern

improved movement with click on repeated testing

ahp

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2
Q

what are the features of browns revolving adduction

A

restriction of elevation in adduction

downdraft on adduction

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3
Q

describe the aetiology of congenital browns

A

short anterior sheath

developmental anomaly affecting trochlea/superior oblique complex

ineleastic superior oblique tendon

nodule or swelling on the tendon

lr pulley instability

in the ccdd spectrum

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4
Q

what are congenital cranial dysinnervation disorders

A

cfeom- Congenital fibrosis of eom

3rd, 4th , 5th , 6th

moebius syndrome

Duane syndrome

brown syndrome

ocular synkinesis syndrome

horizontal gaze palsy with progressive scoliosis

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5
Q

what is the aetiology of acquired browns

A

superior oblique tuck

injury to trochlea area

swelling on tendon

rheumatoid conditions

lr instability

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6
Q

what would you find on investigation for a browns

A

visual acuity - usually normal unless associated manifest deviation

ahp - chin elevation , tilt to affected side and turn to unaffected side

ct- often binocular in primary position possible hyophoria / exophoric

may have reduced control become manifest without ahp

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7
Q

what are the two main parts of the investigation

A

Binocular Function
Usually good binocular functions
Test for potential BSV if manifest
Plot field of BSV in older child or adult

Measurement
PCT in p.p.
May measure on versions and elevation
Plot Hess chart in older child

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8
Q

what is the differential diagnosis for browns syndrome

A

Inferior Oblique Palsy
Muscle sequelae present
A pattern
Negative FDT

Double Elevator Palsy
Elevation limited in all elevated positions
No alphabet pattern
FDT may be negative dependant on aetiology

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9
Q

what are the management options for browns

A

Observe
75% show spontaneous improvement (Dawson et al 2009)

Surgery: Indicated if decompensating, mkd AHP or poor cosmesis
Results often disappointing

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10
Q

what are the surgery options for browns

A

Tenotomy with preservation of intermuscular connective tissue septum

Tenotomy with removal of intermuscular connective tissue septum

Superior Oblique tendon expander

Recession of contralateral S.R.

Reverse S.O. tuck

Operate on horizontal muscles if large
horizontal angle

Tendon Splitting Moghadam (2014) Dubinsky-Pertzov et al(2021)

Trochlea reconstruction in acquired Brown’s

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11
Q

what are the non surgical management options for browns

A

Steroid Injection
To reduce inflammatory reaction or prevent fibrosis in trauma
Some success in early onset (Trimble 1988) though not sustained

Exaggerated Traction Test
Squirrell et al case report in congenital Brown’s. Performed under GA & steroid injection given following traction test. Repeated 5months later

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12
Q

what are the key features of browns

A

restrcition of elevation in adduction

no development of muscle sequelae

often improvement / resolve

surgery only if symptomatic

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