Bone/CF

Question 1

CF: Kalydeco

Answer 1

Ivacaftor
CFTR Potentiator
>1 month

Question 2

CF: Symdeko

Answer 2

Tezacaftor/Ivacaftor
>6 years
Liver

Question 3

CF: Orkambi

Answer 3

Ivacaftor/Lumacaftor
>1 year
BIRTH CONTROL Interaction

Question 4

CF: Trikafta

Answer 4

Elexacaftor/Tezacaftor/Ivacafor
>2 years
LFT q Every Month

Question 5

CF: Alyftrek

Answer 5

Once a day pill
LFT q every month
>6

Question 6

CF: Treatment Drugs

Answer 6

MSSA, MRSA,
P.Aero CHOSE two

Question 7

CF: Maintance Treatment
Dornase Alfa

Answer 7

> 6 inhaled

Question 8

CF: Maintance Treatment
Hypertonic Saline

Answer 8

> 6 years old
can go down
BID

Question 9

CF: Maintance Treatment
Inhaled Mannitol (Bronchitol)

Answer 9

> 18

Question 10

CF: Inflammatory drugs

Answer 10

Azithromycin (with pseduomonas)
or
Ibuprofen

Question 11

CF: Inhaled ABs

Answer 11

Tobramycin, Aztronam USED IN CHRONIC

Question 12

CF: Pancretitis dose

Answer 12

500-2500 units of lipase per meal
10,000 u max kg/day

Question 13

Bones: Osteomyelitis TX

Answer 13

MSSA IV with MRSA 4-8 Weeks
Amputation 1-2 days

Question 14

Bones: Septic Arthritis TX

Answer 14

Cant Dissect
MSSA (Cefazoline, Ceftiaxone, Cefepime, zoysn, unasyn, Meropenem, Ciprofloxacin, Levo) + MRSA

Question 15

Bones: Prosthetic Joint TX

Answer 15

Debridement
1-stage
2nd stage

Pathogen directed + RIFAMPIN based on severity
No RIFAMPTIN for Amputation