Biochem Flashcards

1
Q

Deficiency of Phenylalanine hydroxylase

A

PKU

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2
Q

Coenzymes that transfer acyl groups and active aldehydes

A

TPP, Lipoic acid, Coenzyme A

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3
Q

Coenzyme for amino group transfer

A

Pyridoxal Phosphate

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4
Q

Activation and transfer of CO2

A

Biocytin

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5
Q

Transfer of one carbon compounds

A

Tetrahydrofolate

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6
Q

Transfer for Alkyl group

A

Cobamide B12

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7
Q

Synthesized from Biopterin

A

Tetrahydrobiopterin

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8
Q

Tetrahydrobiopterin involved in hydroxylation reactions catalyzed by

A

Phenylalanine hydroxylase
Tryptophan hydroxylase

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9
Q

Vuygyug

A

Guygyug

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10
Q

Tumor of adrenal medulla

A

Pheochromocytoma

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11
Q

Pathology of Pheochromocytoma

A

Salt and pepper chromatin

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12
Q

MC source of extra adrenal Pheochromocytoma

A

Organ of Zuckerkandl

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13
Q

3 enzymes catalyzed reactions that require TPP

A

Pyruvic acid decarboxylase
Transketolase
Pyruvate dehydrogenase

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14
Q

Pyridoxal Phosphate involved in Amino Acid Reactions

A

Transamination
Decarboxylation
Racemization

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15
Q

Inhibited by Isoniazid

A

Pyridoxal Phosphate

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16
Q

Tetrahydrofolic acid: inhibited by folate antagonists e.g

A

Methotrexate, sulfonamides