AVSD Flashcards
what is a partial canal defect
ostrium primum defect with complete cleft of the AL of MV
what is the gooseneck deformity of the LVOT
because there is apical displacement of the AVV plane , usually because some portion of the ventricular part of the AV septum fails to come up, the LVOT is apically displaced. Sometimes there is some chordal attachment or muscle that obstructs the LVOTO
what is a transitional av canal defect
a partial av canal with a pressure restrictive vsd, sometimes with LVOTO because of chordal attachments from the AL of the MV to the septum
what is the definition of a CAVC
primum asd, unrestrictive inlet vsd and common AVV
what is a Rastelli A (most common)
complete division of the superior common leaflet with chords in the correct places, vsd is small
what is a Rastelli B (rare)
will have dominance defined by straddling chords from the other side (so RV dominance has straddling chords from the MV component over to the RV)
what is a Rastelli C (25%)
undivided superior leaflet without any chord attachment
what is Rastelli C frequently associated with
TOF
in AV canal defects where is the coronary sinus and AV node
inferiorly displaced
where is the bundle of his in av canal defects
in the crest (inferior) border of the defect
what trisomy is frequently associated with CAVC
21
is LVOTO frequent in CAVC with downs
no
Partial and transitional canal defects have a natural history similiar to simple ASD
true
Down’s kids have floppy airways and so they tend to have a pronounced acceleration in PVR and Pa HTN
yes
EKG axis for CAVC
counterclockwise
