ASD, VSD, Tetralogy Flashcards

1
Q

primum ASD

A

incomplete fusion of septum primum & the AV endocardial cushions

common in down syndrome

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2
Q

secundum ASD

A

most common

excessive resorption of septum primum or interrupted septum secundum development

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3
Q

patent foramen ovale

A

incomplete fusion of septum secundum & septum primum

  • those in hypercoagulable state at increased risk for stroke d/t emboli being pushed into systemic circulation
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4
Q

sx & PE findings with ASDs

A

sx: exertional dyspnea, heart failure
PE: systolic ejection murmur, fixed split S2

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5
Q

what do you see on ECG with ASDs?

A
  • incomplete or complete RBBB
  • RAD in secundum ASD (LAD in primum)
  • RVH
  • R atrial enlargement
  • Afib or flutter
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6
Q

what do you see on CXR with ASDs?

A
  • enlarge pulmonary arteries
  • increased pulmonary vascularity
  • enlarged R ventricle
  • enlarged R atrium
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7
Q

transthoracic echo with ASDs

A

saline injection w/ bubble contrast can demonstrate R to L shunt ; pulsed & color flow doppler

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8
Q

TEE

A

transesophageal echo
-used if transthoracic echo quality is not optimal

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9
Q

who should be treated with ASDs?

A
  • left to right shunts over 1.5:1
  • leads to RV volume overload if left untreated
  • pulm HTN precludes closure if pulm systolic pressure > 2/3 of systemic systolic pressure
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10
Q

complications of untreated septal defects

A
  • Afib
  • heart failure
  • paradoxical systemic embolization
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11
Q

Down’s Syndrome & heart defects

A
  • AtrioventricularSD 45%
  • VSD 35%
  • ASD 8%
  • patent ductus arteriosus 7%
    -Tetralogy of Fallot 4%
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12
Q

type A, outflow tract VSD

A

rare; in ventricular septum directly below the pulmonary valve

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13
Q

type B, membranous VSD

A

in membranous septum, in upp ventricular septum, near valves ; most commonly operated on

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14
Q

type C, inlet VSD

A

near atrioventricular canal

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15
Q

type D, muscular VSD

A

in the lower muscular portion of ventricular septum; most common VSD; large # of them close spontaneously

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16
Q

complete AVSD

A

central endocardial cushion defect allows blood to flow b/n all 4 heart chambers / one common atrioventricular valve instead of separate valves

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17
Q

most commonly occurring congenital heart defect

18
Q

VSD in a baby presentation

A

poor eating, failure to thrive, fast tachypnea, dyspnea, easy tiring

19
Q

VSD in a child presentation

A

dyspnea on exertion, not gaining weight, dyspnea when eating or crying

20
Q

VSD in adult presentation

A

dyspnea on exertion, orthopnea, irregular heart beat, fatigue/weakness

21
Q

small shunt VSDs

A

loud, harsh holosystolic murmur in left 3rd & 4th interspaces along the sternum

22
Q

large shunt VSDs

A

RV volume & pressure overload, pulmonary regurg
- late finding of cyanosis

23
Q

what do you see on ECG with VSDs

A

right, left or biventricular hypertrophy

24
Q

what do you see on CXR with VSDs

A

LVH, left atrial enlargement, enlarged pulmonary arteries & increased pulmonary vascularity

25
what pressure makes a VSD inoperable?
PA pressure/systemic pressure greater than 0.67 is inoperable
26
large VSD prognosis
heart failure / survival beyond 40 years is unusual without tx
27
surgical management of VSD
- left to right shunt greater than 1.5 & pulm systolic pressure less than 2/3 of systemic systolic pressure
28
list some cyanotic heart diseases
- tetralogy of fallot - transposition of the great arteries - truncus arteriosus - tricuspid atresia
29
transposition of the great arteries
aorta & pulmonary artery switch places -detected prenatally or shortly after birth -prompt surgical correction
30
truncas arteriosus
normal mitral & tricuspid valves but only 1 valve b/n aortic & pulmonic valves - needs prompt surgical correction
31
tricuspid atresia
hypoplastic R ventricle - tx w/ prostaglandin to maintain patent ductus arteriosis to supply blood to the lungs
32
Tetralogy of Fallot
VSD with R ventricular outflow obstruction secondary to infundibular stenosis - RVH - overriding aorta in 50%
33
Tetralogy severities
- lesser obstruction: left to right shunt, allows for oxygenation - great obstruction: right to left shunt, cyanosis
34
congenital disorders associated with Tetralogy
- Down's syndrome - DiGeorge syndrome -velocardiofacial syndromes
35
PE findings with Tetralogy
- crescendo-decrescendo harsh systolic ejection murmur - loudest at left mid to upper sternal border - radiates posteriorly - normal S1 & single S2 d/t diminished P2 - cyanosis of lips & nail beds
36
Tet spells
- hypercyanotic episodes precipated by sudden increase in R to L shunting of blood elicited by feeding/crying - squatting releases this
37
what do you see on ECG with Tetralogy
-RVH -RAD -RBBB after repair -QRS > 180 msec
38
what do you see on CXR with tetralogy
- boot shaped heart - prominent R ventricle - concave R ventricular outflow tract - enlarged R sided aorta sometimes
39
Tetralogy echo pre repair
- unrestricted VSD - R ventricular infundibular stenosis - enlarged aorta
40
Tetralogy echo post repair
- pulm valve regurg - R ventricular & L ventricular function - aortic regurg
41
types of repair for Tetralogy
- VSD patch - RV outflow tract patch - takedown of arterial-pulmonary artery shunt
42