ARVC

Question 1

What are the MAJOR echocardiographic criteria for ARVC?

Answer 1

Regional RV akinesia, dyskinesia or aneurysm and one of the following; [either PLAX RVOT ≥ 32mm (≥ 19mm/m2)/PSAX RVOT ≥ 36mm (≥ 21mm/m2)] OR fractional area change ≤ 33% (even in the presence of normal RVOT size).

Question 2

What are the MINOR echocardiographic criteria for ARVC?

Answer 2

Regional RV akinesia or dyskinesia and one of the following; [either PLAX RVOT ≥ 29 - < 32mm (≥ 16 - <19mm/m2)/PSAX RVOT ≥ 32 - < 36mm (≥ 18 - < 21mm/m2)] OR fractional area change > 33 - < 40% (even in the presence of normal RVOT size).

Question 3

RVOT pLAX and pSAX should be measured where in the cardiac cycle?

Answer 3

At end diastole.

Question 4

True or false; the presence of TR is not a sensitive or specific finding for ARVC.

Answer 4

True.

Question 5

RVOT measurements from which view have been found to be more reproducible, the pLAX or pSAX?

Answer 5

pSAX.

Question 6

Enlargement of the PA makes the diagnosis of ARVC less or more likely (and why)?

Answer 6

Less likely (may be indicative of conditions such a pHTN).

Question 7

What is not specific for ARVC but may support the diagnosis in the presence of other findings?

Answer 7

A thickened or echo-bright moderator band.

Question 8

What measurement suggest RV thinning (with regards to wall thickness)?

Answer 8

<3mm.

Question 9

RV akinesia, dyskinesia or aneurysm are diagnostic criteria for ARVC in the presence of what?

Answer 9

RV dilatation or reduced RV fractional area change.

Question 10

Patients with ARVC present how?

Answer 10

With ventricular arrhythmias or sudden cardiac death.

Question 11

True or false; ARVC is hereditary.

Answer 11

True.