ANEMIA 3 Flashcards

1
Q

TRIADA DE ANEMIA HEMOLITICA

A

ICTERICIA, ANEMIA Y ESPLENOMEGALIA

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2
Q

CUALES SON AS ANEMIAS HEMOLITICAS INTRACRPUSCLARES POR AFEC DE LA MEMB

A

ESFEROCITOSIS

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3
Q

CUALES SON LAS ANEMIAS HEMOLITICAS INTRACORPUSCULARES POR AFECT DE ENZIMAS

A

DEF 6 GLU FOS DESHIDROGENAS

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4
Q

CUALES SON LAS ANEMIAS HEMOLITICAS INTRACORPUSCULARES POR AFEC DE HB

A

TALASEMIAS Y FALCIFORMES

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5
Q

ANEMIA HEMOLITICA HEREDITARIA MAS FREC

A

ESFEROCITOSIS HEREDITARA

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6
Q

CUALES SON LAS ANEMIA HEMOLITICAS HERDITARIAS

A

INTRACORPUSCULARES

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7
Q

DEFECTO EN ESFEROCITOSIS HEREDITARIA

A

DEF DE ANKIRINA

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8
Q

CARACT DE ESFEROCITOSIS HEREDITARIA

A

ANEMIA MICROCI HIPERCROMICA, (ESFEROCITOS)

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9
Q

DX DE ESFEROCITOSIS HEREDITARIA

A

HEMOLISIS OSMOTICA

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10
Q

COMPLICACIONES EN ESFEROCITOSIS HEREDITARIA

A

CRISIS ANEMICAS POR INF POR PARVOVIRUS B19

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11
Q

DEFECTO EN LA ELIPTOCITOIS HERIDATIRA

A

DEFECTO EN LA ESPECTRINA

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12
Q

DX DIF DE LA ELIPTOCITOS ESFEROCITOSIS HERDITARIA

A

ADMEAS DE LA FORMA DE LOS ERITROCITOS….LA ELIPTOCITOSIS NO ES POSTIVA EN PRUEBA DE FRAGILIDAD OSMOTICA

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13
Q

PORQE SE DAN CRISIS HEMOLITICAS EN G6PDH

A

POR FAVISMO O FAMRACOS COMO NITRO, FENAZO, SULFAS, PRIMAQUINA DAPSONA

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14
Q

HERENCIA DE DEF G6PDH

A

LIGADA A X CR X

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15
Q

QUE HEMOGLOBINOPATIA SE HACE TAMIZ

A

DE G6PDH A LOS 3-5 DIAS CON ESPECTOMETRIA

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16
Q

ESTUDIO MAS SENSIBLE PARA VLORAR LA ELASTICIDAD O DEFORMIDAD ERITROCITARIA

A

ECTACITOMETRIA

17
Q

CARACT DE LAS TALASEMIAS

A

MICROCITICA HIPOCROMICA

18
Q

HB BART

19
Q

HB H

20
Q

CR DONDE SE PRODUCE LA TALASEMIA ALFA

21
Q

CR DE LA TALASEMIA BETA

22
Q

ELECTROFORESIS DE HB NORMAL

A

A1 FORMADA POR 2ALFA Y 2 BETA, A2 Y F E NPEQUEÑA CANTIDAD

23
Q

MORFOLOGIA DE LOS ERITROCITOS EN TALASEMIAS

A

TIRO AL BLANCO ( NO PATOGNOM)

24
Q

CLASIF DE TALASEMIA ALFA

A

AFEC 1 GEN: ASINTOMATICO SOLO RASGO….2 GENES: TALASEMIA MENO2, 3 GENES HB H GRAVE, 4 GENES TALASEMIA MAYOR CON HYDROPS FETAL

25
TALASEMIA HETEROCIGOTA
TALASEMIA BETA MENOR
26
TALASEMIA HOMOCIGOTA
TALASEMIA BETA MAYOR
27
QUEIN FORMA LA HB F
2 ALFA MAS 2 GAMMA
28
QUIEN FORMA LA HB A2
2 ALFA MAS 2 DELTA
29
QUIEN DEFINE LA GRAVEDAD DE LA TALASEMIA BETA
LA HB F ENTRE MAS MAS GRAVE
30
FISIOPATO DE LAS TALASEMIAS
DEFECTO EN LA FORMACION E GLOBINA
31
SINONIMO DE TALASEMA BETA MAYOR
ANEMIA DE COOLEY
32
CLINICA DE LA TALASEMIA BETA MAYOR
HIPERPLASIA DE MO CON MALF OSEAS COMO CRAENO EN CEPILLO
33
SINONIMO DE ESFEROCITOSIS HEREDITARIA
MINKOWSKI CHAUFFARD