Acyanotic CHD - CAVSD

Question 1

A CAVSD is formed by

Answer 1

An ostium primum defect that overlies the mitral and tricuspid valves

Question 2

CAVSD: In most instances, a cleft is found in what valve

Answer 2

Anterior leaflet of the mitral valve

Question 3

CAVSD is common in children with what syndrome

Answer 3

Down syndrome

Question 4

Definitive surgical procedure for CAVSD

Answer 4

Fontan procedure

Question 5

Basic abnormality in CAVSD with ostium primum defect

Answer 5

L-R shunt across the AVSD and mitral insufficiency

Question 6

CHD: Normal or accentuated 1st heart sound, wide fixed splitting of S2, pulmonic SEM sometimes preceded by a click, low-pitched, mid-diastolic rumbling murmur at the left lower sternal border or apex or both

Answer 6

CAVSD

Question 7

Low-pitched, mid-diastolic rumbling murmur at the left lower sternal border or apex or both is due to

Answer 7

Increased flow through the AV valves

Question 8

CHD: Superior orientation of the mean frontal QRS axis with left axis deviation to the left upper or right upper quadrant

Answer 8

CAVSD

Question 9

In CAVSD, Q waves are seen in what leads

Answer 9

I and aVL

Question 10

CHD: Abnormally low position of AV valves on echo, with encroachment of the mitral valve on the left ventricular outflow tract

Answer 10

CAVSD

Question 11

CHD: Gooseneck deformity of the LV outflow tract

Answer 11

CAVSD

Question 12

Surgical intervention MUST be performed during infancy in CAVSD, as early as 6-12 months of age because

Answer 12

Risk of pulmonary vascular disease