acquired disorders connective tissue

Question 1

name for well defined furrows at base of neck

Answer 1

cutis rhomboidalis nuchae (CRN)

Question 2

What is favre-Racouchot

Answer 2

confluent plaques studded w comedones

often symmetrical, periorbital though can be unilateral

Question 3

what the the single/multiple papules on ears called that are considered variant/presentation of solar elastosis

Answer 3

elastotic nodules of the ear

Question 4

Name of the condition over lateral aspects of index finger/first web space/ ulnar aspect of thumb - due to chronic friction/photodamage

Answer 4

collagenous + elastotic marginal plaques (CEMP) of the hands

Question 5

DDx for collagenous + elastotic marginal plaques of the hand

Answer 5

Remember BMAFS CT + CDAG for focal keratodermas

Marginal papular keratodermas (acroelastoides, focal acral hyperkeratosis, spiny keratoderma)

Question 6

DDx of colloid milia

Answer 6

Adult colloid milium (multiple, symmetrical, assoc w sun expoure)
Juvenile colloid milium (onset pre-puberty, familial, secondary to UV-ind degeneration of KCs)
Nodular colloid degeneration (usually solitary on face/scalp/chest)
Acrokeratoelastoides of Costa (hands + feet, black skin)
Collagenous + elastotic marginal plaques of the hand
Nodular amyloid

Question 7

What are non-UV related causes of cutaneous atrophy?

Answer 7

Steroids Strip Poikilodermatous Scars Away And (FLA) (always) Heal Promptly + Properly

• corticosteroid atrophy
• striae
• poikiloderma
• atrophic scars
• acrodermatitis chronicum atrophicans
• atrophodermas (FLA - follicular, linear, atrophoderma of Pasini + Perini)
• paroxysmal haematoma of finger
• panatrophy
• Parry-Romberg

Question 8

Risk factors for striae?

Answer 8

Pregnancy, rapid growth in adolescence, steroid use (oral/topical), Marfan’s, Cushing

Question 9

What are inherited poikiloderma syndromes?

Answer 9

Kindler
Dyskeratosis Congenita
Bloom
Rothmund Thompson
Cockayne
Acrogeria

Question 10

what are acquired causes of poikiloderma?

Answer 10

poikiloderma of Civatte
Post XRT/heat/cold
poikilodermatous MF
post inflammatory (eg LP
systemic autoimmune (DM, LE, systemic scleerosis)