3 - Cardiomyopathies Flashcards
What is the second MC cause of SCD in teens and the leasing cause of death in competitive athletes?
Hypertrophic cardiomyopathy
The primary cardiomyopathies:
Slide 7 long list
Common causes of secondary cardiac myopathies
Slide 8 - long list
Clinical features and ECG for dilated cardiomyopathy?
Congestive heart failure
Chest pain
Regurgitant murmurs
LVH, poor R-wave progression
Clinical features and ECG for myocarditis?
Fever
Tachycardia
Myalgias
CP
Nonspecific ST-T wave changes, often with pericarditis
Clinical features and ECG for HOCM
DOE CP Palpitations Syncope Prominent J wave Pulsus bisferiens Systolic ejection murmur (increases with valsalva and decreases with squatting)
LVH, large septal Q waves
Usual cause of dilated cardiomyopathy?
Idiopathic
What is the primary indication for cardiac transplant in the US?
Dilated cardiomyopathy
Risks for dilated cardiomyopathy
black, male, age 20-50
Majority have advanced dz by the time of presentation
Describe dilated cardiomyopathy?
Systolic and diastolic dysfunction and diminished LV and RV contractile force, resulting in low CO and increased end-systolic and end-diastolic ventricular volumes
Hallmarks of dilated cardiomyopathy?
LV (and often RV) dilation accompanied by normal LV wall thickness
Sxs of dilated cardiomyopathy?
Looks like CHF
DOE Orthopnea PND Bibasilar rales Dependent edema
Why CP with dilated cardiomyopathy?
Limited coronary vascular reserve rather than atherosclerotic dz
Clinical features of dilated cardiomyopathy
Impaired valve closure
Holosystolic mitral or tricuspid regurgitant murmurs at LLSB
Enlarged liver and pulsatile if tricuspid insufficiency is significant
Dx of dilated cardiomyopathy?
Not usually made in the ED
Typically made at follow-up via echo
CXR with dilated cardiomyopathy
Enlarged cardiac silhouette and increased cardiothoracic ratio
MC findings on ECG for dilated cardiomyopathy?
LV hypertrophy and left atrial enlargement
Also, a-fib is common
How urgent is the echo with dilated cardiomyopathy?
Driven by patient presentation
Get it when:
Cause of HF is uncertain
To exclude known causes of HF that may be correctable
To estimate ejection fraction
To R/O other potential complications that may be amenable to therapy
What improves pt survival in cardiomyopathy pts?
ACE inhibitors
Blockers
Carvedilol
Dilated cardiomyopathy pts with ventricular ectopy may benefit from:
Amiodarone
Implanted pacemaker defibrillator
ED txt for dilated cardiomyopathy 2/2 noncompliance
Nitrates
IV diuretics
Re-start normal meds
Patient counseling
Make sure you r/o severe issues, as well (i.e. possible ischemia)
LVAD?
Awesome and weird device for severe dilated cardiomyopathy patients - moves the blood for em
Hallmarks of HCM?
On echo -> asymmetric septal hypertrophy and histologic hypertrophy associated with myocardial fiber disarray surrounding areas of increased loose CT