Sjögren Syndrome

Question 0

Type of RTA associated with Sjögren syndrome

Answer 0

Type 1 (distal) RTA

Question 1

Most common causes of secondary Sjögren syndrome (2)

Answer 1

RA, SLE

Question 2

Most common type of lymphoma in Sjögren syndrome

Answer 2

Extranodal marginal zone B cell lymphoma of the mucosa-associated lymphoid tissue (MALT)

Question 3

Sensitivity and specificity of classification criteria for Sjögren syndrome

Answer 3

Both 94%

Question 4

Stain used to reveal corneal lesions consistent with dryness in Sjögren syndrome

Answer 4

Rose Bengal stain

Question 5

Two viral infections that are part of the exclusion criteria for Sjögren syndrome

Answer 5

Hepatitis C, HIV

Question 6

Primary cause of increased mortality in Sjögren syndrome

Answer 6

Lymphoma

Question 7

Clinical and serologic markers associated with lymphoma development in Sjögren syndrome (4)

Answer 7

Palpable purpura, low C4 levels, mixed monoclonal cryoglobulinemia, persistent parotid gland enlargement

Question 8

Percentage of patients with extraglandular involvement in Sjögren syndrome

Answer 8

50%