Causes
Idiopathic- primary HTN (young people)
Secondary- Chronic Lung disease or LHD
Caused by recurrent PTE
Congenital Heart Disease- shunt
Symptoms
Dyspnoea on exertion
Syncope/ Pre Syncope on exertion
Chest tightness
Signs
Raised JVP Right ventricular heave Loud second pulmonary heart sound Hepatomegaly Ankle oedema
Investigations
ECG
ECHO- detect fault in tricuspid valve
CXR- enlarged blood vessels
national pulmonary vascular unit- RH catheterisation, cardiac output.
Treatment
Treat underlying cause (HTN, lung disease)
Give anticoagulation and diuretics and O2
CCB
Prostacyclin
ERA (endothelium receptor antagonist)
CTEPH
lung/heart transplant.