HRS IA 2013

Question 1

LQT: Indications for Beta blockers (2)?

Answer 1

Asymptomatic with QTc > 470 msec

Symptomatic for syncope OR documented VT/VF

Question 2

LQT: When is Left cardiac sympathetic denervation indicated (2) ?

Answer 2

ICD is refused

BB are not effective or are refused

Question 3

LQT: When to implant ICD (1) ?

Answer 3

Survivors of Cardiac Arrest

Question 4

Three ways to diagnose LQT (Definite) ?

Answer 4

• Schwartz score > 3.5
• Pathologic Gene mutation
• > 500 msec over repeated ECGs with no secondary cause

Question 5

2 ways to diagnose Brugada Pattern?

Answer 5

• Type 1

- Type 2: Provocative change to type 1

Question 6

3 lifestyle recommendations for BrS?

Answer 6

• Avoid Brugada drugs
• Treat fever
• Avoid excessive ETOH intake

Question 7

Indication for ICD in BRS?

Answer 7

VT/VF/Syncope

Question 8

Who gets BB with CPVT?

Answer 8

All symptomatic patients

Question 9

Who gets ICD in CPVT?

Answer 9

OHCA/Recurrent syncope/VT despite optimal management

Question 10

How to diagnose SQT (2) ?

Answer 10

QTc < 330 msec

QTC < 360 msec with pathogenic mutation or family history of SQTS

Question 11

How to diagnose PCCD?

Answer 11

Progressive conduction system disease in patients < 50 years old with no structural heart disease or myopathies.

Question 12

How to diagnose CPVT?

Answer 12

• Age < 40, no other reason for VT and bidirectional VT
• Pathogenic mutation
• If Bidirectional VT and FDR with CPVT

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Question 13

What is gene responsible for CPVT?

Answer 13

RYR2 gene

Question 14

What should be done for Sudden Unexplained Death syndrome? (2)

Answer 14

• Family history

- Autopsy