CYSTIC FIBROSIS Flashcards

1
Q

What is cystic fibrosis

A

genetic disorder affecting lungs, pancreas, liver, intestine + reproductive organs

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2
Q

symptoms associated with CF

A
  • viscous sputum
  • chest infections
  • malabsorption
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3
Q

Tx of CF

A
  • mucolytic = dornase alfa
  • long-term antibacterial considered to supress chronic staph.aureus
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4
Q

Why is dornase alfa given

A

aids clearance of mucus/sputum from lungs

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5
Q

what is given if nutrition and exocrine pancreatic insufficiency

A

pancreatin

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6
Q

Aim of CF tx

A

prevent lung infections and maintain lung function

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7
Q

Monitoring CF

A
  • liver disease
  • diabetes
  • bone density
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