CYSTIC FIBROSIS Flashcards
1
Q
What is cystic fibrosis
A
genetic disorder affecting lungs, pancreas, liver, intestine + reproductive organs
2
Q
symptoms associated with CF
A
- viscous sputum
- chest infections
- malabsorption
3
Q
Tx of CF
A
- mucolytic = dornase alfa
- long-term antibacterial considered to supress chronic staph.aureus
4
Q
Why is dornase alfa given
A
aids clearance of mucus/sputum from lungs
5
Q
what is given if nutrition and exocrine pancreatic insufficiency
A
pancreatin
6
Q
Aim of CF tx
A
prevent lung infections and maintain lung function
7
Q
Monitoring CF
A
- liver disease
- diabetes
- bone density