Congenital Lung Disease

Question 1

Features of CCAM

Answer 1

1. Absent bronchial cartilage
2. Absent bronchial glands
3. Tall columnar mucinous epithelium
4. Proliferation of terminal bronchioles without alveoli and lobar enlargement that causes secondary compression

Question 2

How many types of CCAM are there ?

Answer 2

Type I:
Most severe , large cysts and disorganized lung parenchyma involving multiple lobes
Type II:
Multiple evenly spaced cysts that rarely exceed 1.2cn
Type III:
Bulky firm mass that usually encompass rarely larger than 0.5 Cn

Question 3

Type 1 CCAM

Answer 3

Multiple large cysts or occasionally a single large one surrounded by smaller
Disorganized lung parenchyma
Involves multiple lobes