Cardiomyopathy Flashcards
Which cardiomyopathy is classified as reduced contractility and variable degree of diastolic dysfunction? and what is it associated with with?
Dilation of left ventricle ; SYNDROMIC Diverse array of associated conditions, especially muscular dystrophies: Emery-Dreifuss muscular dystrophy, limb-girdle muscular dystrophy, Duchenne/Becker muscular dystrophy; Laing distal myopathy; Barth syndrome; Kearns-Sayre syndrome
In which cardiomyopathy is it classiffied as normal ventricular size but reduced contractility?
Non-dilated left ventricular cardiomyopathy
What is the pathology of Arrhythmogenic right ventricular cardiomyopathy (ARVC)?
Island of fatty replacement;fibrosis
What are the systemic conditions associated with with ARVC?
Palmoplantar keratoderma, wooly hair
in Naxos syndrome
What is the EKG in Arrhythmogenic Right Ventricular Cardiomyopathy
Inverted T waves in right precordial leads (V1, V2, and V3)
And
Epsilon wave (reproducible low-amplitude signals between end of QRS complex to onset of T wave) in right precordial leads (V1–V3
What is the hallmark of ARVC?
Fibrofatty replacement
What is beck’s triad?
JVD
Muffled distant heart sounds
Low blood pressure
Left sided heart failure symptoms?
Fatigue
Exercise intolerance
Dyspnea
Prthopnea
PND
Weight gain
Peripheral edema
Right sided heart failure symptoms?
Fatigue
Exercise intolerance
Abdominal distention
Left leg swelling
Right sided heart failure signs?
Elevated JVP
Hepatomegaly
Ascites
Lower limb edema
Left sided heart failure signs?
Pulsus paradoxus level and def
Fabry disease is associated which type of cardiomyopathy
Hypertrophic CM
Which CM is characterized by myocyte hypertrophy with disarray?
Hypertrophic CM
